Bone Tumor, desmoplastic fibroma of the sacrum. Case Report
DOI:
https://doi.org/10.29166/rfcmq.v50i2.7450Keywords:
desmoplastic fibroma, sacrum, , resection, removal, intraoperativeAbstract
Introduction: Desmoplastic fibroma is a rare entity, representing less than 0.1% of primary bone tumors. It has a locally aggressive behavior with a tendency to recurrence, ranging from 25% to 72%, when there is incomplete surgical resection.
Objective: To describe the case of a patient with a diagnosis of desmoplastic fibroma of the sacrum, highlighting the importance and relevance for the medical literature, due to the clinical presentation and atypical location, as well as the low prevalence among bone tumors.
Case presentation: We present a 28-year-old female patient with long-standing moderate lumbosacral pain, radiating to the right lower limb and accompanied by paresthesias. Imaging tests and CT-guided biopsy confirmed the diagnosis of desmoplastic fibroma. She received surgical treatment: surgical resection with intraoperative emptying of the residual cavity tumor, with favorable evolution.
Discussion: Desmoplastic fibroma is an infrequent pathology, which requires an adequate complementary management through imaging studies, with specific histopathological confirmation by biopsy. Surgical treatment with wide resection reduces the risk of recurrence.
Conclusions: Desmoplastic fibroma is an infrequent pathology, which requires an adequate complementary management through imaging studies, with specific histopathological confirmation by biopsy. Surgical treatment with wide resection reduces the risk of recurrence.
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