Sacral desmoplastic fibroma: relevance of its contribution to current scientific evidence
DOI:
https://doi.org/10.29166/rfcmq.v51i1.8423Keywords:
Desmoplastic Fibroma, Sacrum, Benign Bone Tumors, Surgical Resection, Differential DiagnosisAbstract
Desmoplastic fibroma is an extremely rare benign bone tumor with locally aggressive behavior. Sacral involvement is exceptionally uncommon. To comment and complement a case of sacral desmoplastic fibroma, providing additional clinical, imaging, histopathological, and therapeutic information based on existing literature. Previous reports of sacral desmoplastic fibroma were reviewed, including cases with synchronous multifocal involvement, clinical presentations, imaging findings, differential diagnoses, and surgical management options. The review highlights the significant diagnostic challenges of sacral involvement, due to its clinical and radiologic similarity to malignant lesions and other benign bone tumors. The complementary role of computed tomography, magnetic resonance imaging, histopathological, and immunohistochemical studies (FOSL1) is emphasized. Wide surgical resection remains the treatment of choice, with long-term follow-up required due to high recurrence rates. The review provides valuable evidence that contributes to expanding knowledge of this rare entity and supports an appropriate diagnostic and therapeutic approach.
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Copyright (c) 2026 Andy Hermógenes Luque-Loor, José André Cedeño-Orejuela, Ariel Melis-Sosa, Paola Ceciliana Añazco-Moreira, Gema Paola Zambrano-Zambrano, Silvia Cristina Pino Andrade
This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.
