Oral rehabilitation in patients with ectodermal dysplasia: one year follow-up
Keywords:
Oral rehabilitation in children, Hypohidrotic Ectodermal Dysplasia, Total AnodontiaAbstract
Ectodermal Dysplasia (ED) are genetic disorders determined by genetic factors, which can change the ectodermal struc-tures such as the teeth, skin, hair, nails, sweat and sebaceous glands. There are many variations of ED, and the Hypohi-drotic or Anhidrotic Ectodermal Dysplasia which is linked to the X chromosome (XLHED) is the best-known form and one of which the dental care is a very important stage of the treatment. This study aimed to report a clinical case of a male patient, 02 years old, suffering from XLHED, whose treatment consisted of making a Total Prosthesis in both arches, with the intention of improving his aesthetic, functional and psychological conditions. This patient sought, with his mother, the baby clinic of the University Santa Cecilia (UNISANTA) with the major complaint of “lack of teeth from birth.” The result was the recovery of aesthetic, functional and psychological conditions of the patient. In view of this, it was concluded that early diagnosis and treatment are important factors to improve the aesthetic, functional and psychological conditions of the child, allowing their physical, emotional and social development. In addition, installation of the Total Prosthesis allowed better nutrition and broke the finger-sucking habit, representing a satisfactory alternative for the rehabilitation treatment.
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